Abstract

Granulosa cell tumors (GCT) of ovary is a malignant tumor originating from sex cord stromal cells. It accounts for 2%-5% of all ovarian cancers. The granulosa is classified separately in adult and juvenile pattern by clinical presentation and histologic characteristics. The juvenile type granulosa cell tumor (JGCTs) are extremely rare. The incidence of JGCTs on the GCTs is 6.2% [1,2]. It is diagnosed in young women and pre-pubertal girls at stage I disease. The literature is scanty. The guidelines of the optimal management are still controversial [3,4]. The prognosis of JGCT is excellent because of tumour recurrence or metastasis being rare. However, JGCT is regarded as a low-grade malignant neoplasm. There is a significant propensity for recurrence or metastasis. Recurrent or metastatic AGCT can manifests many years after initial surgery.