Abstract

Desmoid-type fibromatosis are rare, locally aggressive, benign tumors of soft tissue origin [1]. They compose 0.03% of all neoplasms and less than 3% of all soft tissue tumors. Desmoid tumors often appear on the extremities or external abdominal wall [2]. Desmoid tumors commonly affect people between the ages of 15 and 60 and have a slightly higher incidence in women [1]. These tumors have a high local recurrence rate and have a high potential to infiltrate surrounding organs, although they lack malignant potential [3]. Between 5% and 15% of desmoid tumors have been associated with cases of familial adenomatous polyposis, a genetic condition involving mutations in the APC gene [4].